The differential diagnosis of LCH includes other unilateral intranasal masses such as nasal polyp, antrochoanal polyp, angiomatous polyp, cavernous hemangioma, juvenile angiofibroma, hemangiopericytoma, hemangioendothelioma, paraganglioma, schwannoma, meningocele, meningoencephalocele, glioma, angiosarcoma, lymphoma, Kaposi sarcoma, olfactory neuroblastoma, and vascularized metastases.2,3,8,9Because LCH does not regress spontaneously,3the treatment of choice is total excision. Even if surgery can be performed through an endoscopic or external approach, endoscopic surgery is currently considered the criterion standard for the treatment of both small and large LCHs.6This surgical technique is less invasive, does not alter skeletal growth, avoids aesthetic damage, and allows good control of bleeding. Our patient's LCH was successfully removed with a diode laser through a transnasal endoscopic approach, with no perioperative complications. In conclusion, nasal LCHs are rare in the pediatric population. To our knowledge, the present case represents the youngest child described to date. Imaging studies are mandatory in cases involving large lesions. Radical excision by endoscopic sinus surgery is the ideal treatment for nasal LCH.